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KMID : 0383820080640050369
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Tuberculosis and Respiratory Diseases
2008 Volume.64 No. 5 p.369 ~ p.373
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A Case of Multiple Micronodular Pneumocyte Hyperplasia of the Lung in a Man with Tuberous Sclerosis
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Nam Dong-Hyug
Choi Yoon-Jung
Lee Ju-Hyun
Na Hyoung-Jung
Kim Dong-Hwan
Kim Chong-Ju
Lee Sun-Min
Hong Yong-Kook
Han Chang-Hoon
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Abstract
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Tuberous sclerosis (TS) is an autosomal dominant disorder that is characterized by cutaneous lesions, seizures, mental retardation and hamartomas in various organs including the skin, kidney and brain. Pulmonary involvement is extremely rare, and occurs in approximately 0.1 to 1% of TS cases. Recent reports have indicated multiple micronodular pneumocyte hyperplasia (MMPH) as another rare form of pulmonary involvement of tuberous sclerosis. We report a case of a 35 year-old-male patient who had no pulmonary symptoms but showed multinodular pulmonary shadows on his chest CT scan. The patient was finally diagnosed with TS with MMPH of the lung. MMPH does not appear to have any malignant potential but the clinical significance of MMPH in TS patients is unknown. (Tuberc Respir Dis 2008;64:369-373)
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KEYWORD
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Tuberous sclerosis, Multiple micronodular pneumocyte hyperplasia
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